SUSPEITE DE FlBROSE PULMONAR (FP): SAlBA COMO AGlR
Ao identificar os sintomas de Fibrose Pulmonar, é preciso encaminhar prontamente o paciente para um especialista em pulmão¹. A doença, que pode ser progressiva e fatal², deve ser tratada o quanto antes.
A GRAVIDADE DA FIBROSE PULMONAR
Uma ameaça comum para pacientes de Doenças Pulmonares lntersticiais e de Doenças do Tecido Conjuntivo, a Fibrose Pulmonar é grave e pode ser fatal3-13. Ainda não há cura, mas é possível retardar a progressão dos sintomas. Por isso, o diagnóstico precoce é fundamental.
Tempo mediano de sobrevivência3-13:
Doença Pulmonar lntersticial lndiferenciada - 1 a 2 anos
Fibrose Pulmonar idiopática - 3 a 5 anos
Doença Pulmonar lntersticial associada á Esclerose Sistêmica
- 4 a 6 anos
Doença Pulmonar lntersticial associada á Artrite Reumatoide
- 3 a 7 anosPneumonite por Hipersensibilidade Crônica - 4 a 7 anos
Suspeitou da Fibrose Pulmonar?
Faça o encaminhamento rapidamente.
Por causar danos irreversíveis ao pulmão14-17, a Fibrose Pulmonar diminui a independência e a qualidade de vida dos pacientes. Por isso, é preciso ficar atento aos sintomas, especialmente em pacientes reumatológicos.
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Wells AU, Brown KK, Flaherty KR, et al. What's in a name? That which we call lPF, by any other name would act the same. Eur Respir J. 2018;51(5):1800692.
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Molina-Molina M, Aburto M, Acosta O, et al. lmportance of early diagnosis and treatment in idiopathic pulmonary fibrosis. Exp Rev Resp Med. 2018;12(7):537-539.